2000, Number 6
<< Back Next >>
Arch Cardiol Mex 2000; 70 (6)
Atrioventricular discordance. Ten years experience.
Alva C, Jiménez S, David F, Ortegón J, Sánchez A, Jiménez D, Ledesma M, Argüero R
Language: Spanish
References: 26
Page: 561-568
PDF size: 202.73 Kb.
ABSTRACT
Objective: To know the incidence of ventriculoarterial connections combined with atrioventricular discordance, associated lesions and surgical results, including the first case with anatomical correction.
Method: All patients with atrioventricular discordance by echocardiography from 1990 to March 2000 were analized.
Results: Thirty six patients with atrioventricular discordance were found. Ages ranged from 0.1 to 46 years, with a mean 9.2 years (SD 5.9 years). Atrial chambers were situs solitus in 88.9%, inversus in 11.2%. The ventriculoarterial connections were discordant in 28 (77.7%), double outlet right ventricle in 4 (11.1%) (one of them was a “criss cross” heart), single outlet (pulmonary atresia) in 4 (11.1%), and double outlet left ventricle in 1 (2.7%). Associated lesions: Ventricular septal defect with pulmonary stenosis or atresia was present in 21 (58%), ventricular septal defect with no pulmonary obstruction was observed in 10 (28%). Five had tricuspid regurgitation with right ventricular disfunction, (two adults). Surgical results: 22 (61%) required 28 surgical procedures: 8 (36%) were palliative and 19 (86%) were corrective, one of them was our first anatomical correction. Operative mortality in all was 40.1%, postoperative atrioventricular block was observed in 9 (40.1%).
Conclusion: Right ventricular dysfunction is not uncommon. Surgical results revealed high mortality and high pacemaker requirement for atrioventricular block.
REFERENCES
Lev M, Rowaltt UF: Pathological anatomy of mixed levocardia. A review of thirteen cases of atrial or ventricular inversion with or without corrected transposition. Am J Cardiol 1961; 8: 216-63.
Allwork SP, Pentall HH, Becker AE, Cameron H, Gerlis LM, Wilkinson JL, et al: Congenitally corrected transposition of the great arteries: Morphologic study of 31 cases. Am J Cardiol 1976; 38: 910-23.
Anderson RH, Becker AE, Arnold R, Wilkinson JL: The conducting tissues in congenitally corrected transposition. Circulation 1974; 50: 911-23.
Attie F, Miranda I, Zabal C, Buendía A, Casanova JM: Aspectos de interés en la transposición corregida de las grandes arterias. Arch Inst Cardiol Mex 1992; 62: 345-350.
Attie F, Soni J, Ovseyevitz J, Muñóz-Castellanos L, Testelli MR, Buendía A: Angiographic studies of atrioventricular discordance. Circulation 1980; 62: 407-15.
Lundstrom U, Bull C, Wyse RK, Somerville J: The natual and “unnatural” history of congenitally corrected transposition. Am J Cardiol 1990; 65: 1222-9.
Yeh T Jr, Connelly MS, Coles JG, Webb GD, McLaughlin PR, Freedom RM, et al: Atrioventricular discordance. Results of repair in 127 patients. J Thorac Cardiovasc Surg 1999; 117: 1190-1203.
Westerman GR, Lang P, Castaneda AR: Norwood WI. Corrected transposition and repair of associated intracardiac defects. Circulation 1982; 66(Suppl): I 197-202.
McGrath LB, Kirklin JW, Blackstone EH, Pacifivo AD, Kirklin JV, Bargeron LMJ: Death and other events after cardiac repair in discordant atrioventricular connection. J Thorac Cardiovasc Sug 1985; 90: 711-28.
Sano T, Riesenfeld T, Karl TR, Wilkinson JL: Intermediate term outcome after intracardiac repair of associated cardiac defects in patients with atrioventricular and ventriculoarterial discordance. Circulation 1995; 92 (Suppl I): 1272-8.
Szulfladowicz M, Horvath P, de Leval M, Elliot M, Wyse R, Stark J: Intracardiac repair of lesions associated with atrioventricular discordance. Eur J Cardiothorac Surg 1996; 10: 443-8.
Termignon J, Leca F, Vouhé PR, Vernant F, Bical OM, Lecompte V, et al: “Classic” repair of congenitally corrected transposition of the great arteries and ventricular septal defect. Ann Thorac Surg 1996; 62: 199-206.
Connelly Ms, Lui PP, Williams WG, Webb GD, Robertson P, McLaughlin PR: Congenitally corrected transposition of the great arteries in adult: functional status and complications. J Am Coll Cardiol 1996; 27: 1238-43.
Peterson RJ, Frunch RH, Fajman WA, Jones RH: Comparison of cardiac function in surgically corrected and congenitally corrected transposition of the great arteries. J Thorac Cardiovasc Surg 1988; 96: 227-36.
Ilbawi MN, DeLeon SY, Backer CL, Duffy CE, Muster AJ, Zales VR, et al: An alternative approach to the surgical management of physiologically corrected transposition with ventricular septal defect and pulmonary stenosis or atresia. J Thorac Cardiovasc Surg 1990; 100: 410-5.
Yagihara T, Kishimoto H, Isobe F, Yamamoto F, Nihigaki K, Matsuki O, et al: Double switch operation in cardiac anomalies with atrioventricular and ventriculoarterial discordance. J Thorac Cardiovasc Surg 1994; 107: 351-8.
Imai Y, Sawatari K, Hoshino S, Ishihara K, Nakasawa M, Momma K: Ventricular function after anatomic repair in patients with atrioventricular discordance. J Thorac Cardiovasc Surg 1994; 107: 1272-83.
Alva C, Horowitz E, Ho SY, Rigby ML, Anderson RH: The feasibility of complete anatomical correction in the setting of discordant atrioventricular connections. Heart 1999; 81: 539-45.
Franco Vázquez JS, Perez-Treviño C, Gaxiola A: Corrected transposition of the great arteries with extreme counterclockwise torsion of the heart. Acta Cardiol 1973; 28: 636-43.
Attie F, Muñóz-Castellanos L, Ovseyevitz J, Flores-Delgado I, Buendía A, Kuri J, et al: Crossed atrioventricular connections. Am Heart J 1980; 99: 163-72.
Espino-Vela J, De la Cruz MV, Muñoz-Castellanos L, Plaza L, Attie F: Ventricular inversion without transposition of the great vessels in situs inversus. Br Heart J 1970; 32: 292-303.
Acar P, Sidi D, Bonnet D, Aggoun Y, Bonhoeffer P, Kachaner J: Maintaining tricuspid valve competencein double discordance: a challenge for paediatric cardiologist. Heart 1998; 80: 479-83.
Gelatt M, Hamilton RM, McCrindle BW, Connelly M, Davis A, Harris R, et al: Arrhytmia and mortality after the Mustard procedure: a 30-year single-center experience. J Am Coll Cardiol 1997; 29: 194-201.
Cochrane AD, Karl TR, Mee RB: Staged conversion to arterial witch for late failure of the systemic right ventricle. Ann Thorac Surg 1993; 56: 854-62.
Hwang B, Bowman F, Malm J, Krongard E: Surgical repair of congenitally corrected transposition of the great arteries. Results and follow up. Am J Cardiol 1982; 50: 781-5.
Williams WG, Suri R, Shindo G, Freedom RM, Morch JE, Trusler GA: Repair of major intercardiac anomalies associated with atrio-ventricular discordance. Ann Thorac Surg 1981; 31: 527-32.