Durán PMA, Olivares MK, Aristi UG, Soriano RJ

Language: Spanish
References: 17
Page: 200-204
PDF size: 272.13 Kb.

ABSTRACT

A case of a 6 year old boy with congenital cyanotic cardiopathy and heart congestive failure is reported. He was autopsied and the heart showed Ebstein’s anomaly with right ventricle hypoplasia. The most valuable morphologic finding was the downward displacement of the tricuspid orifice with fusion of the septal and posterior cusp with the right ventricle wall. The differential diagnosis must be made with others cardiopathies that have right ventricular hypoplasia like Uhl’s anomaly and right ventricular dysplasia. We reviewed the differential diagnosis between the heart anomaly with partial or diffuse absence of the right ventricle.

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