2012, Number 2
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Rev Med MD 2012; 3.4 (2)
Pediatric Wilms Tumor with Intracardiac and Intracaval Extension. Case Report
Medina-Andrade MA, López-Taylor JG, Gutiérrez-Ureña JA, Aguirre-Jáuregui ÓM, Jiménez-Fernández C, García-Martínez JA, Zúñiga-Gordillo R
Language: Spanish
References: 7
Page: 132-135
PDF size: 567.55 Kb.
ABSTRACT
Wilms tumor is the most frequent kidney neoplasia in pediatric patients, and it can be associated with blood vessel
extension, particularly to the renal vein and inferior vena cava; it has been reported that 1% of these tumors can invade
right cardiac cavities in spite of preoperative chemotherapy. In addition to a literature review, we present the case of a
patient diagnosed with Wilms tumor and extension to superior vena cava and right atrium demonstrated by
echocardiographic imaging; in which after being treated unsuccessfully with a combination of chemotherapy and
radiotherapy was managed surgically with tumor mass excision and extracorporeal circulation.
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