Pacheco LRC, Torres GB, Ugalde VJA, Vecchyo CC, Sastré ON

Language: Spanish
References: 14
Page: 152-156
PDF size: 163.28 Kb.

ABSTRACT

Among the cartilaginous tumors, the enchondromas and osteochondromas are benign lesions formed by mature hyaline cartilage that affect the tubular bones of the hand and most commonly, the middle and proximal phalanges, and can be multiple o single lesions. When the enchondromas appear in the early childhood, are multiple lesions with no specific hereditary pattern, are known as Ollier's disease. Another feature of this disease is the unilateral appearance, affecting mainly hands and feet. In this article we present the case of a 18 years old male, with diagnosis of Ollier's disease since he was 2 years old, with affection of both hands and feet, most severely affected in the right upper extremity. The patient was treated with functional aesthetic amputation of 4th and 5th fingers and tumor resection of 2nd and 3rd fingers of his right hand. There are very few cases reported in the literature with such a severe deformity of the hand, and in spite of what have been described previously, in this case, the disease has not been self limited, to the contrary, it has recurred even more aggressively each time, now affecting the four extremities, thus raising the chance of malignant transformation, which makes indispensable to have a close follow up of the patient for a long time.

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