Jiménez-Fernández CA, Bautista-González S, Guzmán-Chávez OR, García Negrete E, Ramírez Cedillo David, López-Taylor JG

Language: Spanish
References: 10
Page: 222-225
PDF size: 678.83 Kb.

ABSTRACT

13 years old male patient with no relevant medical history begins, 2 months prior to admittance, with mild dyspnea and 2 bradycardia. An echosonogram is asked for reporting a 13.6cm² lump in the left auricle (LA) bulging to mitral valve causing mild failure, 38mm LA and 67% ejection fraction (EF). The patient undergoes surgery in which is observed a encephaloid tumor with insertion to back wall of LA and extension to the posterior mitral valve with a base of 5 cm and 8x5cm diameter. A complete extraction and histopathological study is performed reporting malignant schwannoma through immunohistochemistry with presence of S100 protein. The heart malignant schwannoma is a tumor originated in the heart branches of the vagus nerve and the cardiac plexus; mainly located in the right auricle (RA) next to the interatrial septum, though also found in the left auricle (LA) and occasionally bulges to the same side ventricle. Affects people between 20 and 50 years old and rarely kids. Histologically presents neural differentiation with spindle-shaped cells; the s100 protein, Leu-7 and myelin are immunohistochemical highlighters indicating nervous differentiation. The clinical picture depends on the location, size, growth and speed rate in which is done the diagnostic. The most common symptoms are thoracic pain, dyspnea, arrhythmias, failures in the conduccion, syncope, frequently associated to pericardial effusion.

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