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ISSN 1561-3119 (Electronic)

2012, Number 3

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Rev Cubana Pediatr 2012; 84 (3)

Idiopathic pulmonary hemosiderosis

Rivero GM, Seiglie DF, Luís ÁMC, Pantoja PO, Arencibia NA

Language: Spanish
References: 22
Page: 293-300
PDF size: 64.43 Kb.


ABSTRACT

Idiopathic pulmonary hemosiderosis is those processes characterized by anomalous depots of hemosiderin in the pulmonary parenchyma, secondary to diffuse and repeated alveolar bleedings. It is an unknown disease, uncommon and mostly severe. It occurs in the first decade of life of most of the patients, regardless of sex. Here is a 7 years-old patient, female, Caucasian, with a history of 22 hospitalizations since she was a baby, due to recurrent episodes of respiratory distress diagnosed as bronchial pneumonias associated to acute anemia. For the diagnosis of this disease, bronchoalveolar lavage was performed and hemosiderin-loaded macrophages were observed. The clinical and lab evaluation excluded secondary causes. She was treated with prednisone and she improved her condition. The clinical, diagnosing and therapeutic elements of this disease were discussed.


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