Yabur-Espitia M, Espinola-Zavaleta N

Language: Spanish
References: 14
Page: 65-70
PDF size: 141.82 Kb.

ABSTRACT

Objective: to describe the clinical behavior and the echocardiographic features of six patients with ventricular non-compaction associated to complex congenital heart disease.
Methods: a complete clinical history and the echocardiographic study were performed in six patients with complex congenital heart disease. Jenni´s criteria for the echocardiograph assessment of ventricular non compaction were used.
Results: in all cases prominent trabeculae and deep intertrabecular recesses in the ventricular wall filled by direct blood flow from the ventricular chamber were visualized by color Doppler imaging. The ratio of none compacted to compacted layer was of 2.5 ± 0.19. The associated congenital heart diseases were: Ulh´ s anomaly, the absence of right atrioventricular connection, single ventricle, cleft of mitral valve, transposition of the great arteries, double inlet in left ventricle.
Conclusions: the clinical manifestations were presented in the childhood and they were associated with congenital heart defect. The echocardiography is a diagnostic method which allows the assessment of the ventricular non compaction.

REFERENCES

1. Maron BJ, Towbin JA, Thiene G, Antzelevitch CH, Corrado D, Arnett D, et al. Contemporary definition and classification of the cardiomyopathies. Circulation 2006;113:1807-1816.

2. Elliott P, Andersson B, Arbustini E, Bilinska Z, Cecchi F, Charron P, et al. Classification of the cardiomyopathies: a position statement from the European Society of Cardiology Working Group on Myocardial and Pericardial Diseases. Eur Heart J 2008;29(2):270-276.

3. Markiewicz-Loskot G, Moric-Janiszewska E, Loskot M, Szydlowski L, Weglarz L, Hollek A. Isolated ventricular noncompaction: clinical study and genetic review. Europace 2006;8(12):1064-1067.

4. Ritter M, Oechslin E, Sütsch G, Attenhofer C, Schneider J, Jenni R. Isolated noncompaction of the myocardium in adults. Mayo Clin Proc 1997;72(1):26-31.

5. Jenni R, Oechslin E, Schneider J, Attenhofer Jost C, Kaufmann PA. Echocardiographic and pathoanatomical characteristics of isolated left ventricular non-compaction: a step towards classification as a distinct cardiomyopathy. Heart 2001;86(6):666-671.

6. Goo HW, Park IS. Left ventricular noncompaction in an infant: use of non-ECG-gated cardiac CT. Pediatr Radiol 2007; 37(2):217-220.

7. Cavusoglu Y, Ata N, Timuralp B, Gorenek B, Goktekin O, Kudaiberdieva G, et al. Noncompaction of the ventricular myocardium: report of two cases with bicuspid aortic valve demonstrating poor prognosis and with prominent right ventricular involvement. Echocardiography 2003;20(4):379-383.

8. Espinola-Zavaleta N, Soto ME, Castellanos LM, Játiva- Chávez S, Keirns C. Non-compacted cardiomyopathy: clinical-echocardiographic study. Cardiovasc Ultrasound 2006;4:35

9. Tatu-Chitoiu A, Bradisteanu S. A rare case of biventricular non-compaction associated with ventricular septal defect and descendent aortic stenosis in a young man. Eur J Echocardiogr 2008;9(2):306-308.

10. Stöllberger C, Kopsa W, Finsterer J. Non-compaction of the right atrium and left ventricle in Ebstein’s malformation. J Heart Valve Dis 2006;15(5):719-720.

11. Wessels MW, De Graaf BM, Cohen-Overbeek TE, Spitaels SE, de Groot-de Laat LE, Ten Cate FJ, et al. A new syndrome with noncompaction cardiomyopathy, bradycardia, pulmonary stenosis, atrial septal defect and heterotaxy with suggestive linkage to chromosome 6p. Hum Genet 2008;122(6):595-603.

12. Petersen SE, Selvanayagam JB, Wiesmann F, Robson MD, Francis JM, Anderson RH, et al. Left ventricular noncompaction: insights from cardiovascular magnetic resonance imaging. J Am Coll Cardiol 2005;46(1):101-105.

13. Tynan MJ, Becker AE, Macartney FJ, Jiménez MQ, Shinebourne EA, Anderson RH. Nomenclature and classification of congenital heart disease. Br Heart J 1979;41 (5):544-553.

14. Lilje C, Rázek V, Joyce JJ, Rau T, Finckh BF, Weiss F, et al. Complications of non-compaction of the left ventricular myocardium in a paediatric population: a prospective study. Eur Heart J 2006;27(15):1855-1860.