Ávila RF, Velazco OY, Curbelo RL, Pila PR

Language: Spanish
References: 11
Page: 475-482
PDF size: 110.86 Kb.

ABSTRACT

Background: autosomal dominant polycystic kidney disease is one of the major causes of chronic renal failure in adult population.
Clinical case: a patient with an autosomal dominant polycystic kidney disease is reported, who presented as complications an hepatic cirrhosis of mechanical cause, were repeated virological studies in search of hepatitis B and C, which were negative, presence of collateral circulation in the abdominal wall and tension ascites, hemorrhoids grade III and esophageal varices, all this as an expression of severe liver damage. Also showed the presence of a chronic respiratory insufficiency with restrictive pattern, spirometric and radiological studies carried out, lung compression and diaphragm displacement by the size of kidneys and the great conflict in space was detected, also presented hernias in the periumbilical region and right iliac fossa by the great intra-abdominal pressure this patient suffered. He had episodes of lower digestive bleeding and died because of a brutal hematemesis from esophageal varices.
Conclusions: these are infrequent complications presented in autosomal dominant polycystic kidney disease.

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