Morón GGC, Urrutia TFJ, Fuentes CMC

Language: Spanish
References: 19
Page: 7-12
PDF size: 64.97 Kb.

ABSTRACT

Introduction: West syndrome is characterized by the presence of myoclonic jerks in the form of massive, mental impairment and EEG pattern called hipsiarritmia. It has several etiologies, symptomatic, cryptogenic and idiopathic; the most frequent is the symptomatic form. When diagnosed and treated at an earlier age this type of seizures show a better prognosis for resolution. Objective: Analyze the frequency and factors associated with West syndrome. Material and methods: We retrospectively reviewed records of patients diagnosed with West syndrome in the clinical neurology at the Hospital for Children, Mother and Child Institute of the State of Mexico, from January first, 2008 to December 31, 2010. We analyzed the frequency and risk factors present in patients diagnosed with West syndrome. Results: We found 17 patients with West syndrome. The neonatal pathologies encountered were perinatal asphyxia in five patients (29%), hyperbilirubinemia in five (29%), sepsis in two (11%), tuberous sclerosis in two (11%) and seizures in two (11%). One hundred percent of patients present with symptomatic West syndrome. It was found that when diagnostic earliest form, this type of seizure has a better response to treatment. Conclusions: Knowledge of the clinical manifestations of West syndrome allows more early diagnosis and initiate treatment, improving patient prognosis.

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