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ISSN 1405-1699 (Print)
Órgano Oficial del Colegio Mexicano de Alergia, Asma e Inmunología Pediátrica y de la Asociación Latinoamericana de Pediatría

2011, Number 2

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Alerg Asma Inmunol Pediatr 2011; 20 (2)

Life quality in primary immunodeficiencies

Vargas PA, Bustamante OJC, Muriel VR, Espinosa RF

Language: Spanish
References: 41
Page: 57-64
PDF size: 72.03 Kb.


ABSTRACT

Primary immunodeficiencies are genetic diseases that are characterized by a predisposition to repeated infections, that are usually severe and / or caused by opportunistic microorganisms. They can be life threatening if not diagnosed and treated promptly. Diagnosis delay is often associated with permanent damage to vital organs and disability that are usually proportional to the delay to begin treatment.Thanks to advances in diagnosis and treatment of these diseases, there are more patients every day who survive to adulthood. In recent years there have been developed several instruments to assess quality of life of pediatric patients suffering from chronic diseases. In this article we review the available instruments to assess quality of life in children and about publications using these instruments to evaluate quality of life in patients suffering from primary immunodeficiencies.


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