Palermo MSF, Luscialdo S, Aguilar M,Martínez F, Trigubo D

Language: Spanish
References: 3
Page: 94-98
PDF size: 274.52 Kb.

ABSTRACT

Authors report two cases of Galen Vein congenital defect registered by echographic screening during the third trimester of gestation. Case 1: Non-ecoluccent ultrasound image equidistant to Willis polygon, revealed as a vascular alert sign at Doppler color array. A pulsed Doppler screening confirm assert showing a spinned and turbulent figure which it was diagnosed as a Galen Vein aneurism. A healthy 3,960 g male newborn was delivered by cesarean section and his brain ultrasound study revealed an ecogenic spinned turbulent cyst back to third ventricle. Echocardiogram screening revealed right cavities dilatation and left-right shunt according to media pulmonary hypertension. Regular and dynamic brain MRN revealed a Galen Vein malformation, so, a successful embolization treatment was performed at 8 months of life. Case 2: Fetal evaluation includes an ultrasound screening at 27 weeks which revealed suspicious of a brain vascular defect. After a new and advanced pulsed ultrasound evaluation at 30^th week of gestation, an ascitis, a left pericardium drainage and a right cavities cardiomegalia were registered. Doppler screening revealed umbilical artery reverse shunt and a medium brain artery dilatation. Echocardiogram registered an balanced activity cardiomegalia. Therefore, fetal lung maturity was induced and a cesarean section was performed at 31 weeks of pregnancy after fetal abdomen drainage. A male newborn with 1,744 g, Apgar score 5/8 was delivery. Unfortunately, after a 27 coil vascular treatment, a cardiac distress combined to pleura hemorrage and hepatomegalia were developed. A III and IV ventricle arrest and hydrocephalia were also registered. Newborn dies at 3rd day of treatment. Authors state up-dated information is scarce, however medical treatment must be done when general neonatal health be improved and balanced and let to vascular current procedure be performed.

REFERENCES

1. González RJ, Ceciliano A, Zuccaro G. Malformación de la vena de Galeno. Rev Argen de Neurocienc 2006; 20: 169-72.

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3. Li AH, Armstrong D, TerBrugge KG. Endovascular treatment of vein of Galen aneurismal malformation: management strategy and 21-year experience in Toronto. J Neurosurgery Pediatrics 2011; 7: 3-10.