Fajardo-Ochoa F, Peralta-Valdez I, Jiménez-y Felipe JH, Olivas-Peñuñuri MR

Language: Spanish
References: 14
Page: 67-73
PDF size: 373.74 Kb.

ABSTRACT

Introduction: Congenital cystic adenomatoid malformation (CCAM) is a rare abnormality of lung development. CCAM is a cystic area within the lung that stems from abnormal embryogenesis. An adenomatous overgrowth of the terminal bronchioles with a consequent reduction in alveolar growth occurs.
Case Report: We reported a case history of an infant born with the presentation of respiratory distress like symptoms 8 days after birth. Cystic lesions in right lung were revealing by chest radiography and CT scanning of the thorax. Resection of the affected lobes by lobectomy was made. CCAM Stocker (1977) type II lesions were the histologic findings. Healthy discharged.
Conclusion: Because most CCAM lesions are manageable with the proper assessment, diagnosis, and interventions, it is vital that members of the neonatal health care team be knowledgeable about this malformation.

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