2011, Number 3
Congenital adrenal hyperplasia salt loss. Clinical case
Díaz GNA , Ávalos V, Fragoso RR, Cuairán RV
Language: Spanish
References: 12
Page: 169-174
PDF size: 424.41 Kb.
ABSTRACT
Hereditary disorders related to the adrenal glands, with a deficient production of hormones (cortisol and aldosterone), and an androgen overproduction. Clinical manifestations: hypotension, anorexia, nausea, abdominal pain, hyperpigmentation of skin folds and palm lines. Girls present: ambiguous genitals, pubic, axillary and facial hair, hoarse voice, abnormal menstrual periods. Boys present precocious development, alterations in genitals, pubic and axillary hair. Oral manifestations are: hyperpigmentation around the lips, mucosa and gingival margin. A clinical case is presented of a six-year old female patient diagnosed with salt losing CAH or CAH seeking treatment at the Hospital Infantil de México Federico Gómez (HIMFG) (Federico Gomez Mexico s Children Hospital ). The dental department specialist sought inter-consultation with the Endocrinology Department in order to plan a dental treatment for the patient. Treatment consisted of stainless steel crowns and extraction of primary teeth. Pits and fissures sealants were applied, brushing techniques were taught and fluoride gel was applied. As an anti stress preventive measure, the patient´s daily steroid dose was adjusted to avoid acute adrenal failure. The patient s hypertensive medication was not suspended. Amoxicillin (50 mg) was used an hour before the procedure as an antibiotic prophylactic measure. Multidisciplinary services ensure effective and safe dental procedures.REFERENCES