medigraphic.com
Colegio de Medicos y Cirujanos República de Costa Rica

2010, Number 592

<< Back Next >>

Rev Med Cos Cen 2010; 67 (592)

Síndrome de Mayer-Rokitansky-Kuster-Hauser (Agenesia congénita vaginal)

Chacón BA

Language: Spanish
References: 19
Page: 135-138
PDF size: 424.82 Kb.


Text Extraction

This is a case presentation of a 27-year-old female who presents with primary amenorrhea and congenital vaginal agenesis. The patient was diagnosed with Mayer-Rokitansky-Kuster-Hauser Syndrome. This article reviews the etiology and clinical features of this syndrome, as well as its diagnostic tests.


REFERENCES

  1. ACOG Comité No 274. Nonsurgical Diagnosis and Management of Vaginal Agenesis. Vol 100, No 1, July 2002.

  2. Buttram V, Gibbons W. Mullerian Anomalies: a proposed classification (an analysis of 144 cases). Fertility and Sterility. July 1979; 32(1): 40-46.

  3. Casthely S, Maheswaran C , Levy J. Laparoscopy: An important tool in the diagnosis of Rokitansky Kuster-Hauser syndrome. Am J Obstet Gynecol. 15 june 1974;119(4): 571-572.

  4. Duncan PA, Shapiro LR, Stangel JJ, Klein RM, Addonizio JC. The MURCS association: Mullerian duct aplasia, renal aplasia and cervicothoracic somite dysplasia. J Pediatr 1995, 399-402.

  5. Evans T, Poland M, Boving R. Vaginal malformations. Am J Obstet Gynecol. 15 dec 1981;141(8):910-920.

  6. Fedele et al. Magnetic Resonance Imaging in Mayer-Rokitansky-Kuster-Hauser Syndrome. Obstetrics and Gynecology. Oct 1990; 76(4):593-596.

  7. Fedele L, Stefano B, Giovanni Z, Raffaelli R. Laparoscopic creation of a neovagina in patients with Rokitansky syndrome: analysis of 52 cases. Fertility and Sterility. August 2000; 74(2): 384-389.

  8. Gardo, S, Papp .Z, Gaal J., XO/XX mosaicism in the Rokitansky-Kuster- Hauser Syndrome. The Lancet, dec 18, 1971.

  9. Griffin J, Edwards C, Madden J, Harrod M, Wilson J. Congenital Absence of the Vagina. Annals of Internal Medicine, 1976; 85:224-236.

  10. Laufer R. M. Congenital anomalies of the uterus. UpToDate Vol 12 (2): 2004

  11. Laufer R. M. Congenital anomalies of the vagina. UpToDate Vol 12 ( 2): 2004

  12. Mintz M, Thickman D, Gussman D, Kressel H. MR Evaluation of Uterine Anomalies. AJR . Feb 1987; 148: 287-290.

  13. Nussbaum A, Sanders R, Gearhart J. Obstructed Uterovaginal Anomalies: Demonstration with Sonography. Part I Neonates and Infants. Radiology. 1991; 179:79-83.

  14. Nussbaum A, Sanders R, Gearhart J. Obstructed Uterovaginal Anomalies: Demonstration with Sonography. Part II Teenagers. Radiology. 1991; 179:84-88.

  15. Oppelt P. et al. Clinical aspects of Mayer-Rokitansky-Kuester-Hauser syndrome: recommendations for clinical diagnosis and staging. Human Reproduction. 2006; 21(3):792-797.

  16. Rosenberg H, Sherman N, Tarry W, Duckett J, McCrum H. Mayer- Rokitansky- Kuster-Hauser Syndrome: US Aid to Diagnosis. Radiology. 1986; 161:815-819.

  17. Strubbe et al. Mayer-Rokitansky-Kuster-Hauser Syndrome: Distintion Between Two Forms Based on Excretory Urographic, Sonographic and Laparoscopic Findings. AJR. Feb 1993; 160:331-334.

  18. Tarry W.F, Duckett J, Stephens D. The Mayer Rokitansky Syndrome: pathogenesis, classification and management. The Journal of Urology. Sep 1986; 136:648-652.

  19. Togashi et al. Vaginal Agenesis: Classification by MR Imaging. Radiology 1987; 162:675-677.




2020     |     www.medigraphic.com