Yáñez S, Val-Bernal JF, Riancho JA

Language: Spanish
References: 15
Page: 234-237
PDF size: 160.54 Kb.

ABSTRACT

Elastosis perforans serpiginosa is an infrequent skin dermatosis of unknown aetiology characterized by the transepidermal elimination of abnormal elastic fibres. An increased prevalence of common skin conditions and other peculiar and rare dermatosis such as elastosis perforans serpiginosa has been described in Down´s syndrome. We report herein two women with Down´s syndrome, and elastosis perforans serpiginosa. We review the previous reports of elastosis perforans serpiginosa, the peculiar findings in patients with Down´s syndrome, and possible pathogenetic mechanisms.

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