Cervantes-García IF, Camacho-Muñoz E, Orozco-Pérez J, Gutiérrez-Enríquez R, Aguirre-Jáuregui O

Language: Spanish
References: 5
Page: 79-84
PDF size: 543.48 Kb.

ABSTRACT

Introduction: Rhabdomyosarcoma is a malignant tumor originated in the soft tissues of the body. The areas where houses are commonly head, neck, bladder, vagina, arms, legs and trunk. The prognosis depends on the primary disease site, size, group, and histologic subtype. In cases of localized disease can achieve cure ranges up to 85%. Dr. Fillip et al. reported their experience of 107 children with pelvic rhabdomyosarcoma in 2004, in which the use of combination chemotherapy, radical surgery and urinary diversion with colonic reservoir showed improved survival in these patients.
Case report: Women’s 2 years, started 3 months prior to admission with acute urinary retention, beginning study of the aetiology of imaging studies showing a bladder tumor. Cystoscopy was performed with histopathological biopsy compatible with Rhabdomyosarcoma botryoides of the bladder floor. Run for 3 months based cytoreductive chemotherapy Vincristine, then surgical exploration by finding a bladder tumor covered trigone and urethra, which is done by total exeresis of the bladder, with the formation of reservoir with 20 cm segment of descending colon The histopathological of the surgical specimen confirmed the diagnosis of Rhabdomyosarcoma botryoides with positive margins in anterior vaginal wall. Currently the patient has normal renal function with functional colonic reservoir.
Discussion: Rhabdomyosarcoma is the most common bladder tumor in childhood. Malignant tumors of the bladder arising from connective or mesenchymal tissue are extremely rare. The prognosis for these types of tumors is unfavorable because they tend to recur locally and invade the pelvis, so that radical treatment is indicated early. In rare cases the tumor is confined to the dome of the bladder and can be resected. We have used chemotherapy and radiotherapy to reduce tumor mass, followed if necessary by a surgical procedure such as partial or radical cystectomy with formation of a colonic urinary reservoir.

REFERENCES

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