Sandra Luz Lizárraga-López, Patricia Zárate-Castañón, Alfredo Bobadilla-Aguirre, Ma Eugenia Melgoza-Arcos

Language: Spanish
References: 11
Page: 153-157
PDF size: 560.47 Kb.

ABSTRACT

Primary cardiac tumors are rare in childhood and are mostly benign (97%). Rhabdomyomas are the most frequent benign primary tumors with an incidence of 45% in autopsy series and 19% clinical series. In the pediatric population it incidence is 0.27%. They are benign tumors in view of their histological features. However, they may give rise to clinical manifestations depending on their location and on the structures they involve, obstruct or invade. They are associated with tuberous sclerosis has been observed up to 81% of the patients. We report a case of a newborn male who presented at birth with congestive heart failure (CHF), bradycardia. He was diagnosed as tuberous sclerosis with intracardiac rhabdomyoma which resolved spontaneously. Patient is currently asymptomatic one year after the initial diagnosis.

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