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ISSN 2007-3194 (Print)
Órgano de difusión oficial del Instituto Materno Infantil del Estado de México

2009, Number 3

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Arch Inv Mat Inf 2009; 1 (3)

Pentalogía de Cantrell: presentación de dos casos

Moreno CÁ, Hurtado EG, Rodríguez AG, Cordero GCA, Becerril MT, López SR, Bautista ZA, Vega SMA

Language: Spanish
References: 13
Page: 102-104
PDF size: 88.13 Kb.


ABSTRACT

It is a rare syndrome characterized by a disruption in the lower sternum, ectopia cordis, defect above the diaphragm, abdominal wall defects before supraumbilical, defects in the diaphragmatic pericardium and cardiac abnormalities. We report two patients, primigravid, with echosonography which reported a defect in the abdominal chest wall with protrusion of bowel loops (omphalocele), ectopia cordis, so pentalogy of Cantrell diagnosed.


REFERENCES

  1. Cantrell JR, Haller JA, Ravitsh MM. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium and heart. Surg Gynecol Obstet 1958; 107: 602.

  2. Siles C, Boyd PA, Manning N, Tsang T. Omphalocele and pericardial effusion: possible sonographic markers for the pentalogy of Cantrell or its variant. Obstet Gynecol 1996; 87: 840-842.

  3. Sachis SL, Beltra PR. Cantrell’s pentalogy: complete treatment, step by step. Cir Pediatr 1992; 5: 101.

  4. Tayoma WM. Combined congenital defects of anterior abdominal wall, sternum, diaphragm, pericardium, and heart: a case report and review of the syndrome. Pediatrics 1972; 50: 778.

  5. Denath FM, Romano W, Solez M. Ultrasonographic findings of exencephaly in pentalogy of Cantrell: case report and review of the literature. J Clin Ultrasound 1994; 22: 351.

  6. Peer D, Moroder W, Delucca A. Prenatal diagnosis of the pentalogy of Cantrell combined with exencephaly and amniotic syndrome. Ultraschall Med 1993; 14: 94.

  7. Carmi R, Boughman JA. Pentalogy of Cantrell and associated midline anomalies: a possible ventral midline developmental field. Am J Med Genet 1992; 42: 90.

  8. Bennett TL, Burlbaw J, Drake CK. Diagnosis of ectopic cordis at 12 weeks gestation using transabdominal ultrasonography with color flow Doppler. J Ultrasound Med 1991; 10: 665.

  9. Benacerraf B. Prenatal diagnosis of fetal syndrome. New York: Churchill Livingstone;1998: 267-269.

  10. Moore KL. The development human: clinical oriented embryology. 4th ed. Philadelphia: WB Saunders; 1998.

  11. Abu Y, Wray A, Williamson R. Antenatal ultrasound diagnosis of variant of pentalogy of Cantrell. J Ultrasound Med 1987; 6: 535-538.

  12. Sanders SR. Structural fetal abnormalities: the total picture. Ectopic cordis-Pentalogy of Cantrell. EUA: Mosby; 1996: 68-70.

  13. Yao YH, Chien-CHL, Chi CHC. Prenatal sonographic diagnosis of Cantrell’s pentalogy with cystic hygroma in the first trimester. J Clin Ultrasound 1998; 26: 409-412.




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