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ISSN 0210-5187 (Electronic)

2009, Number 3

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Med Cutan Iber Lat Am 2009; 37 (3)

Elastoris perforans serpiginosa in a patient with Wilson’s disease treated with penicillamine

Almazán-Fernández FM, Abad-Romero J, Hernández-Gil SJ, Naranjo-Sintes R

Language: Spanish
References: 10
Page: 151-153
PDF size: 171.77 Kb.


ABSTRACT

Elastosis Perforans Serpiginosa belongs to perforating diseases of the skin. It is a rare condition that appears in early ages, childhood or early adult age. Almost half of the cases are related to different genetic alterations or prolonged treatments with penicillamine. The lesions are queratotic papules of 2-5mm with serpiginous or annular pattern, and the neck and the flexures are the most frequent locations. The principal anatomopathologic characteristics are hiperplasic and transepidermal elimination of elastic fiber. We show a patient with 48 years old, with Wilson’s disease in treatment with D-penicillamine, who consulted by annular repetitive lesions and spontaneous resolution.


REFERENCES

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