Drut R, Altamirano E, Ollano A

Language: Spanish
References: 22
Page: 20-23
PDF size: 288.24 Kb.

ABSTRACT

Heterotopic adrenal tissue can be found all the way in the migration of the male gonad from the dorsal coelom to its intrascrotal position. Any level of cryptorchidism increases this anomaly. In the present report we refer a patient with the clinical constellation of Coffin-Siris syndrome presenting inguinal hernia and cryptorchidism. The histological examination of the resected testis revealed nodules of adrenal cortex arranged between rete testis ducts and the seminiferous tubules, cells were positive for alpha-inhibin and vimentin. This peculiar adrenal cortex heterotopia seems to have been reported only once.

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