López GL, Asz SD, Vázquez VJA, Gil GJF, Arenas R

Language: Spanish
References: 13
Page: 251-255
PDF size: 151.95 Kb.

ABSTRACT

Erythromelalgia is a syndrome characterized by intermittent redness, increased temperature and burning pain affecting mainly lower extremities; exacerbation of symptoms occur by exposure to heat. We describe a 16-year-old male patient with a year history of recurrent attacks of burning pain, warm and redness affecting the face, chest, hands and feet. Symptoms increase with exposure to heat and present amelioration with cold water. This is a primary erythromelalgia case with spontaneous resolution, previously called idiopathic erythromelalgia.

REFERENCES

1. Drenth JP, Morsche RH, Guillet G, Taieb A, et al. SCN9A mutations define primary erythermalgia as a neuropathic disorder of voltage gated sodium channels. J Invest Dermatol 2005;124(6):1333-8.

2. Paira S, Cassano G, Korol V, Ortiz A, et al. Erythromelalgia with subsequent digital necrosis, glomerulonephritis and antiphospholipid antibodies. J Clin Rheumatol 2005;11(4):209-12.

3. Davis MD, Sandroni P, Rooke TW, Low PA. Erythromelalgia: vasculopathy, neuropathy or both? A prospective study of vascular and neurophysiologic studies in erithromelalgia. Arch Dermatol 2003;139(10):1337-43.

4. Mork C, Salerud EG, Asker CL, Kvernebo K. The prostaglandin E1 analog misoprostol reduces symptoms and microvascular arteriovenous shunting in erythromelalgia. A double-blind, crossover, placebo-compared study. J Invest Dermatol 2004;122(3):587-93.

5. Jeffcoate WJ, Idris I, Game FL. Erythromelia or Mitchell's syndrome-new names for unexplained signs of inflammation in distal symmetrical neuropathy in diabetes. Diabet Med 2004;21(12):1334-8.

6. Hernández DME, Lemm AMC, De Alba AL. Eritromelalgia. Rev Cent Dermatol Pascua 1997;6(1):17-20.

7. Jang HS, Jung D, Kim S, Jo S, et al. A case of primary erythromelalgia improved by mexiletine. Br J Dermatol 2004;151(3):708-10.

8. Flores CC, Espejo RF, Dueñas VA, Ramírez RF. Eritromelalgia: reporte del primer caso a nivel nacional y revisión de la bibliografía. Rev Soc Peru Med Interna 2003;16(1):20-27.

9. Berlin AL, Pehr K. Coxistence of erythromelalgia and Raynaud’s phenomenon. J Am Acad Dermatol 2004;50(3):456-60.

10. Davis MD. Erythromelalgia. Mayo Clin Proc 2004;79(3):298.

11. Ricart JM. Eritromelalgia asociada a trombocitosis esencial. QMC 2002;II(4):45-48.

12. Sano S, Itami S, Yoshikawa K. Treatment of primary erythromelalgia with cyclosprine. N Engl J Med 2003;349(8):816-7.

13. Bravo MM, Iglesias MJM, Pérez MA, Porto JA, et al. Dolor de extremidades. An Esp Pediatr 2002;56(6):589-90.