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2007, Number 4

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Rev Med Hosp Gen Mex 2007; 70 (4)

Idiopathic portal hypertension associated with hepatocarcinoma and colangiocarcinoma. A case report

Cavazos SC, Lazos OM, Aguirre GJ

Language: Spanish
References: 9
Page: 189-193
PDF size: 211.07 Kb.


ABSTRACT

Idiopathic portal hypertension (IPH) is a very rare illness of unknown etiology, it presents a wide range of macroscopic and microscopic changes that go from a macroscopically normal liver to a multinodular, atrophic and cirrhosis-like organ; microscopically the most common changes are flebosclerosis and perivascular fibrosis of the portal system vessels. Most of the patients have splenomegalia and upper digestive tract bleeding. IPH has been reported in Japan, India and in US; there are few cases from Latin America. This is a case of a young male with IPH associated with hepatocarcinoma and cholangiocarcinoma diagnosed by autopsy. The hepatic changes represent the last spectrum of the disease. There is only another case of IPH with hepatocarcinoma reported in the literature, so this is an exceptional case.


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