2022, Number 4
<< Back Next >>
Cir Card Mex 2022; 7 (4)
Aortic valve replacement in pediatric patients with Laubry-Pezzi syndrome
Ortega-Zhindón DB, Flores-Sarria IP, Calderón-Colmenero J, García-Montes JA, Pereira-López GI, Cervantes-Salazar JL
Language: English
References: 12
Page: 70-73
PDF size: 259.03 Kb.
ABSTRACT
Objective. The aim was to evaluate the clinical and surgical
results of pediatric patients with Laubry - Pezzi Syndrome
(LPS) undergoing cardiac surgery.
Methods. An
observational and retrospective study was carried out.
Patients diagnosed with LPS undergoing cardiac surgery
from January 1, 2004 and March 31, 2021, were included;
preoperative characteristics and conditions were
considered.
Results. Six patients were included, with a
mean age of 16.3 ± 0.8 years, being 66.7% women. Had
a previous surgery 33%. In 83.3% of the cases, mechanical
aortic prostheses were used, with an average size of
23 ± 0.8 mm. Perioperative complications included arrhythmias
(83.3%), pleural effusion (83.3%), and major
bleeding (16.7%). Overall survival was 66.7% and 16.7%
reoperation.
Conclusions. The closure of the ventricular
defect and replacement of the aortic valve in pediatric
patients with LPS provides a therapeutic option in patients
where aortic valve repair is not possible or has
been unsuccessful.
REFERENCES
Laubry C, Pezzi C. Traité des maladies congénitales du coeur. Paris: JB Bailliere;1921. Cited by Labury C, Routier D, Soulie P. Les souffles de la maladie de Roger.Rev Med Paris. 1933;50:439-448.
Tweddell JS, Pelech AN, Frommelt PC. Ventricular septal defect and aortic valveregurgitation: pathophysiology and indications for surgery. Semin Thorac CardiovascSurg Pediatr Card Surg Annu. 2006:147-152.
Keane JF, Plauth WH Jr, Nadas AS. Ventricular septal defect with aortic regurgitation.Circulation. 1977;56(Suppl 1):i72-i77.
Martínez-Quintana E, Rodríguez-González F, López-Gude MJ. Laubry-Pezzi syndromewith aortic root dilatation treated with a Bentall and De Bono procedure.World J Pediatr Congenit Heart Surg. 2013;4(3):299-301.
Kaskar A, Shetty V, Reddy C, Shetty D. Aortic valve repair in patients with ventricularseptal defect. J Card Surg. 2021;36(11):4160-4166.
AHA medical/scientific statement. 1994 revisions to classification of functionalcapacity and objective assessment of patients with diseases of the heart. Circulation.1994;90(1):644-645.
Otto CM, Nishimura RA, Bonow RO, et al. 2020 ACC/AHA Guideline for theManagement of Patients With Valvular Heart Disease: A Report of the AmericanCollege of Cardiology/American Heart Association Joint Committee on ClinicalPractice Guidelines. Circulation. 2021;143(5):e72-e227.
Tomita H, Arakaki Y, Ono Y, Yamada O, Yagihara T, Echigo S. Impact of noncoronarycusp prolapse in addition to right coronary cusp prolapse in patients with aperimembranous ventricular septal defect. Int J Cardiol. 2005;101(2):279-283.
Chung KJ, Manning JA. Ventricular septal defect associated with aortic insufficiency:medical and surgical management. Am Heart J. 1974;87(4):435-438.
Jung H, Cho JY, Lee Y. Progression of Aortic Regurgitation After Subarterial VentricularSeptal Defect Repair: Optimal Timing of the Operation. Pediatr Cardiol.2019;40(8):1696-1702.
Salih HG, Ismail SR, Kabbani MS, Abu-Sulaiman RM. Predictors for the Outcomeof Aortic Regurgitation After Cardiac Surgery in Patients with Ventricular SeptalDefect and Aortic Cusp Prolapse in Saudi Patients. Heart Views. 2016;17(3):83-87.
Amano M, Izumi C, Imamura S, et al. Progression of aortic regurgitation after subpulmonicinfundibular ventricular septal defect repair. Heart. 2016;102(18):1479-1484.
Full text