Jiménez-Fernández CA, Masini-Aguilera Í, López-Taylor JG, Feliz-Alcántara D, Medina-Andrade MA, Ramírez-Cedillo D, Peña-Juárez RA, González-Torres HM

Language: Spanish
References: 10
Page: s36-39
PDF size: 245.84 Kb.

ABSTRACT

Introduction: the interruption of the aortic arch is rare pathology with an incidence of 0.003 per 1,000 newborns, up to 14% of patients is associated with DiGeorge's syndrome. It is characterized by a complete separation between the ascending and descending aorta. There are three types; in type A there is an interruption between the origin of the left subclavian artery and the descending aorta; which is irrigated from the pulmonary artery through the ductus arteriosus. Clinical case: we present the case of a 2-day-old newborn who beings with data of cardiogenic shock, on physical examination a second single and stronger noise stands out, significant decrease in pulses in lower limbs compared to upper limbs. Imaging studies confirmed an interrupted aortic arch type A with severe hypoplasia of the aorta. Results: in a medical surgical session, it was decided to perform aortic advancement, among the surgical findings severe hypoplasia of the aorta was observed, requiring placement of a Dacron graft. Conclusions: the interruption of the aortic arch is an infrequent pathology with a high mortality, which depends on the associated anomalies, weight, type of interruption and the type of correction if it is one or two times. And adequate and complete physical examination of all newborns is essential to detect cardiac abnormalities.

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