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2021, Number 2

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RCU 2021; 10 (2)

Pseudo prune belly syndrome with preserved renal function and bilateral testicular descent

Mendoza SLJ, Calviac MR, Guerra RM, Mendoza SKM

Language: Spanish
References: 23
Page: 1-12
PDF size: 366.63 Kb.


ABSTRACT

Prune Belly syndrome is characterized by a classic triad: presence of dilation of the upper urinary tract, absence of abdominal wall muscles and bilateral cryptorchidism. The causes of this disease which is more frequent in men are unknown. Patients with a unilateral or bilateral descent of the testicles, partial or complete abdominal wall deficiency and newborn girls with lax abdominal wall are classified as with pseudo Prune Belly syndrome or incomplete Prune Belly syndrome. This article presents the case of a male patient who is currently two years old. At the patient's birth, a diagnosis of pseudo Prune Belly syndrome was made, a disease whose reported cases are very rare. This is the third diagnosis of Prune Belly syndrome at "William Soler" University Pediatric Hospital, in Havana.


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