2021, Number 4
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Acta de Otorrinolaringología CCC 2021; 49 (4)
Craniofacial monostotic fibrous dysplasia
Carías A, Díaz V
Language: Spanish
References: 14
Page: 315-319
PDF size: 159.80 Kb.
ABSTRACT
Fibrous dysplasia is a slowly progressive, genetically based, benign bone disease characterized
by progressive replacement of normal bone with fibrotic tissue. The process
can affect a single bone or multiple bones (monostotic or polyostotic fibrous dysplasia);
the latter may be associated with syndromic diseases, such as McCune-Albright
syndrome.
Objective to review the diagnosis and treatment of patients with fibrous
craniofacial dysplasia.
Materials and methods a review of scientific articles was carried
out in online indexed journals as a technique for collecting relevant information
in databases such as Cielo, Google Scholar, Scopus, PubMed, and DynaMed, with articles
published in English and Spanish. The review period was limited to June 1, 2020.
The search terms were: “fibrous dysplasia”, “monostotic fibrous dysplasia”, and “craniofacial
fibrous dysplasia”. Obtaining 33 articles.
Conclusion craniofacial monostotic
fibrous dysplasia is a rare disease, mainly affecting the mandible, the maxillary bone,
and the inferior turbinate. It can be asymptomatic or present facial deformities, pain
and visual disorders. Its diagnosis is mainly by imaging studies and biopsy. Surgical
treatment must be well planned in each of the patients, focused on facial deformities,
avoiding visual disorders and is necessary when the lesion is malignant.
REFERENCES
Brucoli M, Garzaro M, Dosio C, Boffano P, Benech A.The surgical management of monostotic fibrous dysplasiaof the inferior turbinate. J Stomatol Oral Maxillofac Surg. 2020;121(4):457-59. doi: 10.1016/j.jormas.2019.10.014.
Chandavarkar V, Patil PM, Bhargava D, Mishra MN. A rare casereport of craniofacial fibrous dysplasia. J Oral Maxillofac Pathol.2018;22(3):406-09. doi: 10.4103/jomfp.JOMFP_211_18
Ventura-Martínez N, Guijarro-Martínez R, Morales-Navarro JD,Solís-García I, Puche-Torres M, Pérez-Herrezuelo HermosaG. Displasia fibrosa craneofacial avanzada: a propósito de uncaso. Rev Esp Cirug Oral y Maxilofac. 2014;36(1):32-7. doi:10.1016/j.maxilo.2012.04.002
Álvarez-Vázquez A, Anes-González G, Fernández-GarcíaN. Isolated fibrous dysplasia of the inferior turbinate. ActaOtorrinolaringol Esp. 2013;64(4):312-3. doi: 10.1016/j.otorri.2011.11.006
López-Arcas JM, Colmenero C, Reyes A, Prieto J, Ruiz-SánchezB, Ortega-Aranegui R. Displasia fibrosa maxilar poliostótica enpaciente tratada con pamidronato: a propósito de un caso. RevEsp Cirug Oral y Maxilofac. 2011;33(2):84-7. doi: 10.1016/S1130-0558(11)70016-8
Tovío-Martínez EG, Urbano del Valle SE, Vergara-HernándezCI, Díaz-Caballero AJ. ¿Displasia fibrosa o fibroma osificante?Caracterización histológica de dos casos inusuales. UniversitasOdontologica. 2019;38(81). doi: 10.11144/Javeriana.uo38-81.dffo
AlMomen AA, Molani FM, AlFaleh MA, AlMohisin AK.Endoscopic endonasal removal of a large fibrous dysplasiaof the paranasal sinuses and skull base. J Surg Case Rep.2020;2020(1):rjz404. doi: 10.1093/jscr/rjz404
Bhattacharya S, Mishra RK. Fibrous dysplasia and cherubism.Indian J Plast Surg. 2015;48(3):236-48. doi: 10.4103/0970-0358.173101
Galiè M, Carnevali G, Elia G, Pedriali M, Clauser LC.Craniomaxillofacial Fibrous Dysplasia: ConservativeTreatment and Maxillary Osteotomy Using the Schuchardt-Kufner Technique. Craniomaxillofac Trauma Reconstr.2018;11(1):54-58. doi: 10.1055/s-0036-1597584
Domingues Pinto M, Gaffrée-Braz G, Gomes-Santos R, PolidoD, Rodopiano-Paixão J, Solé de Melo H. Fibrous Dysplasiain Maxillary Bone: Case Report. Int J Oral Dent Health.2018;4:072. doi: 10.23937/2469-5734/1510072
Bhat V, Kansal K, Krishna SH, Pobbysetty R, Hassan S.Fibrous dysplasia of the middle nasal turbinate: imaging andclinical significance. BJR Case Rep. 2016;2(4):20150296. doi:10.1259/bjrcr.20150296
Florez H, Mandelikova S, Filella X, Monegal A, GuañabensN, Peris P. Significado clínico del aumento de los valoresséricos de FGF-23 en la displasia fibrosa. Med Clin (Barc).2018;151(2):65-7. doi: 10.1016/j.medcli.2017.11.036
DynaMed [Internet]. Ipswich (MA): Servicios de informaciónde EBSCO. 1995. Registro N.º T114506, Displasia fibrosa delhueso; [actualizado el 30 de noviembre de 2018, consultado el1 de junio de 2020]. Disponible en: https://www.dynamed.com/condition/fibrous-dysplasia-of-bone [Verificar enlace, ya queno redirige al contenido mencionado]
Alba-García JR, Armengot-Carceller M, Pérez-FernándezCA, Díaz-Fernández A, Taleb C, Campos-Catalá A, et al. Unaforma excepcional de displasia fibrosa craneofacial: Displasiafibrosa de cornete medio. Acta Otorrinolaringológica Española.2002;53(4):291-4. doi: 10.1016/S0001-6519(02)78312-X