Sánchez-Reyes L, Fanghänel G, Márquez-Cid ME, Salazar RR, Labastida-Sánchez C, Solís-Pérez A, Tusie LMT

Language: Spanish
References: 36
Page: 5-11
PDF size: 63.03 Kb.

ABSTRACT

Maturity Onset Diabetes of the Young is a genetically and clinically heterogeneous subtype of type 2 diabetes, characterized by early onset autosomal dominant inheritance and primary defect in insulin secretion. This article reviews the pathophysiologic basis of MODY, describes its clinical manifestations and discusses its diagnosis.

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