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ISSN 1028-9933 (Electronic)

2021, Number 1

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RIC 2021; 100 (1)

Splenic Kasabach-Merritt syndrome in an adult. Presentation of a case and review of the topic

Piriz-Momblant Á, Portuondo-Bandera L, Luna-Pérez L

Language: Spanish
References: 15
Page: 1-9
PDF size: 423.61 Kb.


ABSTRACT

A 22-year-old male black patient presented with big splenomegaly due to a giant hemangioma of the spleen, showing thrombocytopenia and bleeding disorders. A Kasabach-Merrit syndrome was diagnosed. An anterior total splenectomy was performed, returning the platelet count and coagulation disorders back to normal. His evolution was favorable after 18 months of follow-up. Splenectomy surgical treatment was recommended. The topic was reviewed due to the infrequency of the disease.


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