2022, Number 2
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An Med Asoc Med Hosp ABC 2022; 67 (2)
Sacrococcygeal teratoma: case report and radiological findings
Crespo SD, Septién GJM, García-Rizk JA, Zalles VC
Language: Spanish
References: 16
Page: 156-161
PDF size: 385.11 Kb.
ABSTRACT
Sacrococcygeal teratoma is the most common extragonadal germ cell tumor in newborns. It has a frequency of 1 in 27,000 births. The prevalence in females is 3:1-4:1. Prenatal diagnosis is made during obstetric ultrasound and/or with fetal magnetic resonance, identifying a sacral mass. Postnatally the magnetic resonance helps determine the extent of the mass and plan treatment.
Case report: Female newborn of 38.2 weeks of gestation with an ultrasonographic diagnosis at 12 weeks of apparent sacral defect. At week 26, due to the characteristics of the ultrasound a probable sacral teratoma was reported. At birth, she presented a mass of 2 × 2.5 cm in the sacrococcygeal region with layer bleeding. Neurologically there were no alterations. Pelvis radiography was performed demonstrating integrity of the sacral bodies and posterior arches without apparent alterations. Ultrasound identified a mass with heterogeneous echotexture, areas of solid tissue, cystic and calcifications, with central and peripheral vascularity. Magnetic resonance imaging was performed, observing a heterogeneous sacrococcygeal tumor with a solid component, cystic, fat and calcifications, it measured 4.6 × 2.2 × 3.8 cm, extending from S5-base of the coccyx to the right gluteus, conditioning displacement of the uterus and intestinal loops. The teratoma was resected with a good evolution of the patient.
Conclusion: Early prenatal ultrasonographic diagnosis is essential to assess tumor size and complications. It is important to define the morphological characteristics; a larger pelvic component is associated with a mass effect in adjacent structures. Surgical resection is the mainstay of sacrococcygeal teratoma management.
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