Huamán OAF, Torres RG, Medrano HM, López RRP

Language: Spanish
References: 24
Page: 326-334
PDF size: 413.77 Kb.

ABSTRACT

Muenke syndrome is characterized by developmental delay and sensorineural hearing loss. People with a syndrome may have enamel development defects. However, in people with Muenke syndrome, there is no evidence on the management of the sequelae of these defects. Objective: To describe the management of sequelae of enamel development defects in the operating room with a comprehensive dental procedure in primary teeth in a single sesión. Clinical case: 2 -year -old, male patient with medical diagnosis: Muenke Syndrome and dental diagnosis: Post eruptive fractures of the enamel defect extensión I (‹ 1/3 of the tooth) and II (at least 1/3 but less than 2/3 of the affected tooth) in teeth 63, 73, 72,71, 81, 82, 83 and post- eruptive of the extensión III (more than 2/3 of the tooth is affected) enamel defect of teeth 62 and 52, treatment consisted in: veneers that allowed to restore the post eruptive fractures of lower anterior teeth and composite crowns in teeth 62 and 52. Conclusion: The treatment was considered positive clinically since after six months in the patient with Muenke Sindrome; teeth did not present spontaneous pain, neither fistulas or abscess were observed, nor dental mobility.

REFERENCES

1. Saavedra-Ontiveros MD, Morán-Barroso VF. II. Aspectos clínicos en craneosinostosis. Gac Med Mex. 2003;139(3):236–9.

2. Honnebier MB, Cabiling DS, Hetlinger M, McDonald-Mcginn DM, Zackai EH, Bartlett SP. The natural history of patients treated for FGFR3-associated (Muenke type) craniosynostosis. Plast Reconstr Surg. 2008;121(3):919–31.

3. Yasuda T, Nah HD, Laurita J, Kinumatsu T, Shibukawa Y, Shibutani T, et al. Muenke syndrome mutation, FgfR3 P244R, Causes TMJ Defects. J Dent Res. 2012; 91(7): 683-9

4. Mansour SL, Twigg SRF, Freeland RM, Wall SA, Li C, Wilkie AOM. Hearing loss in a mouse model of Muenke syndrome. Hum Mol Genet. 2009; 18(1):43– 50 12.

5. Murali CN, McDonald-McGinn DM, Wenger TL, McDougall C, Stroup BM, Sheppard SE, et al. Muenke syndrome: Medical and surgical comorbidities and long-term management. Am J Med Genet Part A. 2019; 179(8): 1442–50.

6. MINSA. Resolución Ministerial N° 151-2014/MINSA. 2014;517400–6. Disponible en: ftp://ftp2.minsa.gob.pe/normaslegales/2014/RM151_2014_MINSA_EP.pdf

7. Samra F, Bauder AR, Swanson JW, Whitaker LA, Bartlett SP, Taylor JA. Assessing the midface in Muenke syndrome: A cephalometric analysis and review of the literature. J Plast Reconstr Aesthetic Surg. 2016; 69(9):1285–90

8. Suckling GW. Developmental defects of enamel--historical and present-day perspectives of their pathogenesis. Adv Dent Res. 1989; 3(2):87–94.

9. Ruschel HC, Vargas-Ferreira F, Tovo MF, Kramer PF, Feldens CA. Developmental defects of enamel in primary teeth: highly prevalent, unevenly distributed in the oral cavity and not associated with birth weight. Eur Arch Paediatr Dent. 2019; 20(3):241-248. doi:10.1007/s40368-018-0402-4.

10. Alshehhi A, Al Halabi M, Hussein I, Salami A, Hassan A, Kowash M. Enamel defects and caries prevalence in preterm children aged 5-10 years in Dubai. Libyan J Med. 2020 Dec;15(1):1705633. doi: 10.1080/19932820.2019.1705633. PMID: 31873070; PMCID: PMC6968668.

11. Schüler IM, Haberstroh S, Dawczynski K, Lehmann T, Heinrich-Weltzien R. Dental Caries and Developmental Defects of Enamel in the Primary Dentition of Preterm Infants: Case-Control Observational Study. Caries Res. 2018; 52(1–2):22–31.

12. Masumo R, Bårdsen A, Åstrøm AN. Developmental defects of enamel in primary teeth and association with early life course events: A study of 6 - 36 month old children in Manyara, Tanzania. BMC Oral Health. 2013; 13(1):1–11.

13. Caries EC. Early Childhood Caries: IAPD Bangkok Declaration. Int J Paediatr Dent.2019;29(3):384–6.

14. Alkhtib A, Ghanim A, Temple-Smith M, Messer LB, Pirotta M, Morgan M. Prevalence of early childhood caries and enamel defects in four and five-year old Qatari preschool children. BMC Oral Health. 2016; 16(1):1–7.

15. Caufield PW, Li Y, Bromage TG. Hypoplasia-associated severe early childhood caries a proposed definition. J Dent Res. 2012; 91(6):544–50

16. Atar M, Körperich EJ. Systemic disorders and their influence on the development of dental hard tissues: A literature review. J Dent. 2010; 38(4):296–306.

17. Ghanim A, Silva MJ, Elfrink MEC, Lygidakis NA, Mariño RJ, Weerheijm KL, et al. Molar incisor hypomineralisation (MIH) training manual for clinical field surveys and practice. Eur Arch Paediatr Dent 2017; 18(4):225–42.

18. Del Patrocinio Vargas Román M, Rodríguez Bermudo S, Machuca Portillo G. Tratamiento odontológico bajo anestesia general: ¿Un procedimiento útil en el tercer milenio? (I). Med Oral. 2003; 8(2):129–35.

19. Kim S, Kim EY, Jeong TS, Kim JW. The evaluation of resin infiltration for masking labial enamel white spot lesions. Int J Paediatr Dent. 2011;21(4):241–8. 22.

20. Paris S, Schwendicke F, Keltsch J, Dörfer C, Meyer-Lueckel H. Masking of white spot lesions by resin infiltration in vitro. J Dent. 2013; 41 Suppl 5:e28-e34.

21. De Andrade AKMI, Duarte RM, Medeiros E Silva FDSC, Batista AUD, Lima KC, Pontual MLDA, et al. 30-Month randomised clinical trial to evaluate the clinical performance of a nanofill and a nanohybrid composite. J Dent. 2011; 39(1):8-1

22. Maas JRS, Junior IMF, Lodi CS, Delbem ACB. Differences in loosely bound fluoride formation and anticaries effect of resin-based fluoride varnishes. Int J Paediatr Dent.2013; 23(3):166–72.

23. De Andrade AKM, Duarte RM, Medeiros e Silva FDSC, Batista AUD, Lima KC, De Melo Monteiro GQ, et al. Resin composite class I restorations: A 54- month randomized clinical trial. Oper Dent. 2014; 39(6):588–94.

24. Gaurav Kumar M AV. Crowns in Pediatric Dentistry: a Review. J Adv Med Dent Scie Res 2016; 4(2):41-46.