Calderón-Garcidueñas AL, Sagastegui-Rodríguez JA, Canales-Ibarra C, Farías-García R

Idioma: Español
Referencias bibliográficas: 18
Paginas: 589-594
Archivo PDF: 178.05 Kb.

RESUMEN

Se presenta el caso de un hombre de 50 años originario y residente de Saltillo, Coahuila, México, con síndrome demencial y mioclonías de 15 meses de evolución, que había sido incorrectamente diagnosticado en diferentes instituciones. El electroencefalograma mostró descargas lateralizadas al hemisferio derecho con formación de espigas, poliespigas y ondas agudas con patrón periódico. La biopsia cerebral evidenció encefalopatía espon-giforme, con despoblación neuronal y astrocitosis reactiva. Se revisan los conceptos actuales sobre enfermedad por priones.

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