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2011, Número 2

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Dermatología Cosmética, Médica y Quirúrgica 2011; 9 (2)


Síndrome de Melkersson-Rosenthal: consideraciones sobre su real posición nosológica

Hernández PE, Sánz OJC, Abbas KH

Idioma: Español
Referencias bibliográficas: 39
Paginas: 149-154
Archivo PDF: 371.04 Kb.


RESUMEN

El Síndrome de Melkersson-Rosenthal (SMR) es un trastorno raro, de etiología desconocida. Sus principales características son: edema orofacial recurrente, parálisis facial periférica recidivante y lingua plicata. El hallazgo más importante a la biopsia es la presencia de granulomas no caseificados. Presentamos un caso de SMR en un hombre de 37 años, planteando sugerencias terapéuticas e hipótesis sobre su posición nosológica. ¿Se trata de una auténtica entidad nosológica o es parte de un síndrome complejo?


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