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2012, Número 5

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Acta Pediatr Mex 2012; 33 (5)


Rehabilitación bucal bajo anestesia general en un niño con síndrome de Hallervorden-Spatz. Informe de un caso

Mata-Pérez K, Teja-Ángeles E, Durán-Gutiérrez LA

Idioma: Español
Referencias bibliográficas: 25
Paginas: 227-231
Archivo PDF: 208.05 Kb.


RESUMEN

El síndrome de Hallervorden-Spatz es un raro trastorno neurodegenerativo caracterizado por altos niveles de depósitos de hierro en el cerebro. Los pacientes afectados muestran manifestaciones extra-piramidales y deterioro cognitivo, así como distonías, crisis epilépticas, espasticidad, disartria, rigidez de las extremidades y alteraciones visuales. Se describe el caso de un paciente con este síndrome que tenía múltiples caries y lesiones autoinfligidas de la mucosa del labio inferior y de la lengua durante periodos de intensos espasmos orofaciales. Fue sometido una rehabilitación bucal bajo anestesia general. El tratamiento estomatológico tuvo por objeto brindar confort, promover la higiene, evitar el dolor, y eliminar los focos infecciosos.


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