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Antes Revista del Instituto Nacional de Enfermedades Respiratorias

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2011, Número 1

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Neumol Cir Torax 2011; 70 (1)


Guía para el diagnóstico y tratamiento de las alteraciones respiratorias en las enfermedades neuromusculares
I. Antecedentes de la rehabilitación pulmonar en enfermedades neuromusculares
II. Clasificación general de las enfermedades neuromusculares que cursen con alteraciones respiratorias
III. Fisiopatología de las enfermedades neuromusculares
IV. Diagnóstico de las alteraciones respiratorias
V. Tratamiento
VI. Calidad de vida en padecimientos neuromusculares
VII. Cuidados paliativos
VIII. Situación en México de los pacientes con enfermedades neuromusculares y costos

Idioma: Español
Referencias bibliográficas: 318
Paginas: 5-69
Archivo PDF: 953.36 Kb.


FRAGMENTO

La medicina mexicana tiene una gran deuda con un grupo de pacientes que han sido y, por desgracia, en muchos casos siguen siendo invisibles para el gremio médico. Podemos mencionar la más frecuente y mortal Distrofia Muscular Duchenne (DMD). Desde que su autor, Guillaume Benjamin Armand Duchenne, describió en 1860 la enfermedad, si bien es cierto que ha habido avances importantes relacionados con el conocimiento de su etiología y su fisiopatología, no ha sido así con su tratamiento, menos aún con su prevención, y por lo que se refiere al tratamiento de sus complicaciones, el desinterés ha sido patente.
El consenso para elaborar la Guía para el Diagnóstico y Tratamiento de las Alteraciones Respiratorias en las Enfermedades Neuromusculares se llevó a cabo precisamente debido a la evidente falta de conocimiento sobre las complicaciones respiratorias de estas enfermedades y su tratamiento, lo mismo que a la consecuente falta de registros y estadísticas, todo lo cual ha generado que en los centros especializados se vea con indiferencia a este tipo de pacientes y se les cierren las puertas de la atención médica.


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